Until recently, minimal information on the development of body part identification in young children has been available although several developmental assessments include items that involve pointing to or naming body part. The purpose of this study was to examine the sequence in which body parts are learned and can be identified by very young children. The 360 children who 1-to 5-year-old were tested during the... |
We made clinical and statistical observation of 90 very low birth weight infants who were admitted at Soonchunhyang university hospital during the 6 years period from January 1985 through December 1990. The result obtained were as follows: 1) The incidence of very low birth weight infant during 6 years period was 0.68%, and the mortality rate was 488/1000 very low birth weight infants. 2) There was no obvious... |
A Cyclopia in which the elements of the two eyes are completely or partially fused to form an apparently single eye in the middle of the forehead, is part of an anomaly involving not only the eyes themselves but also the anterior part of the brain and the mesodermal structures in the midline. We have experienced two cases of Cyclopia in twin. The autopsy... |
Cardinal clinical features of trisomy 8 are as follow: Absent patellae; mental retardation; facies notable or its anteverted nose, long philtrum, micrognathia and malformed ears; flexion deformities of the fingers or toes, deep plantar V-shaped cleft between the first and third interdigital web of foot, “pH capitonne”. More than 35 patients have been identified as having trisomy 8. The authors experienced a patient of... |
The measurement of body weight, height and blood pressure, urine sugar, oral glucose tolerance test, S-GOT, S-GPT, cholesterol, triglyceride, HDL-cholesterol, LDL-cholesterol tests were made in 324 severely obese elementary, middle and high school students (218 boys and 106 girls) to know the incidence of complication in these children. . The results were as follow: 1) S-GOT or S-GPT were increased abnormally in 38.3% and fatty livers were... |
Hypoglycemia due to Hyperinsulinism is associated with nesidioblastosis, islet cell hyperplasia or adenoma. We experienced two newborn infants suffering from recurrent attacks of hypoglycemia, they were underwent a subtotal pancreatectomy for suspected islet cell dysmaturation syndrome. No tumor was found, but histology revealed islet cell hyperplasia and nesidioblastosis. After surgery one case who was treated with diazoxide, had persistent hypoglycemia but the other showed normal glucose... |
Meconium peritonitis is a non-bacterial foreign body and chemical peritonitis occurring during intrauterine or early neonatal life as the result of an abnormal communicatiion between the bowel contents and the peritonesal cavity. We experienced two cases of meconium peritonitis, diagnosed in according to the clinical and radiologic features, in two female neonates who had the chief complaint of vomiting and abdominal distention. A brief review... |
The congenital lactic acidosis represent a sizable group of metabolic disorders. They are in all likelihood genetically determined, and they are clearly heterogenous. They may be considered broadly as disorders of pyruvate metabolism in which there are two general categories: defects in gluconeogenesis and defects in pyruvate oxidation. We experienced a case of congenital lactic acidosis in neonate who was diagnosed by urinary organic acid... |
Seven cases of lipoid pneumonia in infant who were admitted to department of pediatrics, Soon Chun Hyang University Hospital from July 1988 to March 1990 were reviewed and analysed. The results were as follows: 1) All cases were taken shark liver oil (squalene®) forcefully in supine position 2) Out of 7, all cases were between the age of 3 months and 6 months, and the male... |
The students had to spend their most of times in school. It was supposed that the lighting of classrooms greatly affected the growth and development and visual acuity of students. The illuminance was measured in 12 classrooms of Chun An city (primary, middle and high school) from July to September, 1989. To evaluate the present status and problems of lighting in classrooms, we analyzed... |
We report cystinuria in siblings. Renal colic, hematuria, dysuria and stone passage were developed in younger brother (4 year 6 month old boy). But the elder sister (6 year old girl) had no specific symptoms nor signs. The identification of the disease was proved by cyanide nitroprusside test and amino acid analysis of urine. In our patients the chromatographic amino acid patterns of urine showed... |
We experienced a case of nonimmunologic hydrops fetalis associated with Down syndrome. The patient had generalized edema with severe scrotal swelling and abdominal distension. A roentgenogram showed bilateral pleural effusion and ascites. The chromosomal study revealed 21 trisomy. On autopsy, there were pleural fluid and ascites as well as pericardial fluid. Small ASD and incomplete lobation of the right lung were detected. Chromosomal abnormalities should always... |
Uriary mass screening program for the detection of proteinuria had been performed for a school- age population in the city of Seoul since 1981. Annually, about half million students, who comprised 3 different age group, corresponding to the averages of 11,14, and 17 years, had been examined. A systematic clinical evaluation was designed for students with proteinuria identified in the mass screening through ’87... |
The pose of this study is to survey the prevalence and trend of obesity at ages 6 to 11 in Seoul from 1984 to 1988. The number of children and adolescents comprised of 5,391 boys and 5,289 girls. Overweight was defined as weight that exceeded the standard weight for height and sex by more than 20% (relaive weight > 120%). The result was as... |
We experienced a case of type A Niemann-Pick disease in 31 month-old female infant. She showed dyspnea, marked hepatosplenomegaly and developmental retardation. Fundoscopic examination revealed cherry red spots in both macula. Autopsy finding revealed that Iiver, spleen, lung, kidney, bone marrow, lymph node and brain were involved. Especially multiple ischemic necrosis were found on cerebral and cerebellar white matter. Generalized muscular atrophy and reticular... |
We experienced a case of neonatal short bowel syndrome due to multiple jejuno-ileal atresia with microcolon. On the 1st day of her life, there were symptoms of vomiting and abdominal distension. The radiological study show multiple dilated intestinalloops and malrotation. On the 4th day of her life, the extensive enterectomy was done. The remaining small bowel consisted of 30 cm of proximal jejunum and distal... |
Islet cell adenoma is a rare cause of severe neonatal hypoglycemia. A newborn infant with severe symptomatic hypoglycemia had persistent hypoglycemia in spite of therapy with parenteral glucose solution. Islet-cell adenoma of mixed islet-acinar type was found when subtotal pancreatectomy was performed at 42 days of age. Following surgery she had a transient hyperglycemia and required isulin for 40 days. She has remained normoglycemic but... |
We experienced a case of fetal alcohol syndrome in 9 day old male neonate who delivered at term. On maternal history, his mother had been drunk as much as 64 to 96 cc of alcohol everyday during first trimester and third trimester. The baby had a small for gestational age, microcephaly, bilateral micro-ophthalmia, short palpebral fissure, shallow philtrum, posterior rotation of helix, vocal... |
Micrognathia, cleft palate and glossoptosis, a combination of anomalies known as Pierre Robin syndrome, causes severe respiratory and alimentary difficulties in affected infants. With appropriate care and treatment, mental development can be made normal. But about 10~25% of children become retarded. We have experienced above case in a female infant, aged 6 months. She was acmitted on account of respiratory... |
The authors experienced a case of staphylococcal scalded skin syndrome in 6 month old male infant and reported with brief review of literatures. His chief complaints on admission were fever, vomiting, and watery diarrhea for one day. On the fourth hospitalization day, generalized erythema was developed which was followed by generalized skin exfoliation and methicillin therapy was started. On the... |
Kasabach-Merritt syndrome is rare disorder which consists of hemangioma and thromobocytopenia occurring in infatns. Two cases of giant hemanioma with thrombocytopenia and anemia are reported with review of literures. It is postulated that the abnormalities resulted from intravascular coagulation within the hemangioma. Those patients were managed with prednisolone administration, blood transfusion and compression with the elastic bandage over the hemangioma.... |
This is a case report of the congenital ileal atresia with disuse microcolon. The patient was a 3 day-old male newborn infant who was admitted in department of pediatrics Soon Chun Hyang Hospital with complaints of persistant vomitings, no meconium passage, and jaundice from a few hours after birth. The diagnosis was established by characteristic clinical features and barium enuma... |
The sella turcica is often the key to intracranial diseases and some endocrine disorders. It is significanly enlarged in hypothyroidism, pituitary tumors, some types of increased intracranial pressure and decreased in size in hypopituitarism. Estimation of the sellar size by naked eye is not scientific and moreover very difficult, especially in the borderline sella, an everyday problem of radiologist and... |
Ferrocholinate, choline citrate iron salt is a new chelate iron which is synthesized by reacting ferric hydroxide with choline dihydrogen citrate. Ferrocholinate is used in the prevention and treatment of microcytic, hypochromic anemias due to iron deficiency. Ferrocholinate does not release high concentrations of free ionic iron in the gastrointestinal tract and clinical reports, although limited, seem to indicate that... |
Because of racial differences in the shape and proportions of the skull, orbital distance and amount of the soft tissues about the eyes, patients should be compared with their own racial norms of interpupillary and canthal distances in diagnosis of hypertelorism or hypotelorism. However normal vaules have not been published yet in Korea. Measurements of 1535 Korean children (Male 756;... |