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Case Report
Adrenaogenital Syndrome with Congenital Adrenal Hyperplasia.
Kyeong Rae Moon, Yeong Bong Park, Sang Gi Kim, Jin Heon Kim, Chang Soo Ra, Jae Hong Seo, Ho Won Hwang
Clin Exp Pediatr. 1985;28(1):78-84.   Published online January 31, 1985
Adrenogenital syndrome is caused by a defect in biosynthesis of adrenal corticoids as a result of deficiency in one of the essential enzymes, most commonly 21-hydroxylase. About 50% of 21-hydroxylase deficiency have salt losing type as a result of aldosterone deficiency. We have experienced a casa of adrenogenital syndrome associated with congenital adrenal hyperplasia (salt losing form) in a 3...
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