All issues > Volume 35(1); 1992

Original Article

J Korean Pediatr Soc. 1992;35(1):26-33. Published online January 15, 1992.

The Study on Extracardiac Anomalies Associated with Congenital Heart Diseases

Kye Hwan KH Seol¹, Kang Won KW Lee¹, Chang Sung CS Son¹, Joo Woo JW Lee¹, Young Chang YC Tockgo¹

¹Department of Pediatrics, College of Medicine, Korea University, Seoul, Korea

Abstract

or vice versa. But any specific association pattern of anomalies have remained unestablished despite of many researcherss efforts. Knowledge of the likely association of CHD and extracardiac anomalies may allow us to expect certain disturbances and to correct them, and lower the mortality and morbidity rates in children with CHD. The authors conducted this study in the hope of establishing a specific pattern of association between extracardic anomalies and CHD by evaluating the frequency of extracardic anomalies associated with CHD. The results obstained were as follows: 1) Of 481 patients with CHD, 90 cases (18.7%) were accompanied by extracardic anomalies. 2) CHD with frequent association of extracardic anomalies were as follows in order of decreasing frequency: malposition, single ventricle, endocardial cushion defect, tetralogy of fallot, complex coarctation of aorta, complex ventricular septal defect, patent ductus arteriosus. 3) The systems involved in extracardic anomalies were as follwos, in order of decraesing frequency; chromosomal anomaly, musculoskeletal system, gastrointestinal system, respiratory system, genitourinary system, and central nervous system.

Keywords :Congenetal heart diseases, Extracardiac anomalies