All issues > Volume 35(3); 1992

Case Report

J Korean Pediatr Soc. 1992;35(3):417-421. Published online March 15, 1992.

A Case of Incontinentia Pigmenti

Soo Young SY Kweon¹, Hyun Joo HJ Choi¹, Gyung Hee GH Kim¹

¹Department of Pediatrics, Ewha Womans University College of Medicine, Seoul, Korea

Abstract

Incontinentia Pigmenti is an uncommon genodermatosis that usually affects female infants. The dermatosis may be only a part of more generalized disorder which may affect with great variability the teeth, the eyes, the bones or central nervous system, or may be associated with other malformations or developmental disturbances. We experienced a case of Incontinentia Pigmenti associated with defect of a eye in neonate. A brief review of related literature is also presented.

Keywords :Incontinentia Pigmenti