All issues > Volume 35(6); 1992

Case Report

J Korean Pediatr Soc. 1992;35(6):816-821. Published online June 15, 1992.

A Case of Agenesis of the Right Lung with H-type Tracheoesophageal Fistula

Yong Seok YS Choi¹, Kyung Hee KH Kim¹, Young Chul YC Ahn¹, Baik Lin BL Eun¹, Kwang Je KJ Beck²

¹Department of Pediatrics, Lee Rha Hospital, Cheong Ju, Korea
²Department of Chest Surgery, Lee Rha Hospital, Cheong Ju, Korea

Abstract

Agenesis of the lung is a developmental defect with complete absence or profound hypoplasia of one or both lung : absence of one lung is more common. Absence of both lung is very rare and is incompatible with life. Unilateral or bilateral agenesis of the lung often associated with the skeletal, cardiovascular, gastrointestinal and genitourinary anomalies. H-type tracheoesophageal fistula in approximately 4% of exophageal anomalies. We experienced a case of agenesis of the right lung with H-type tracheoesophageal fistula in a 1day-old male patient. Thereafter we presented the case with brief review of the related literatures.

Keywords :Agenesis of the lung, H-type tracheoesophageal fistula