All issues > Volume 35(7); 1992

Case Report

J Korean Pediatr Soc. 1992;35(7):978-983. Published online July 15, 1992.

A Case of Prune Belly Syndrome ssociated with Turner Syndrome

Chang Soo CS Oh¹, Sang Muk SM Choi¹, Jae Ock JO Park¹, Chang Hwi CH Kim¹, Sang Jhoo SJ Lee¹

¹Department of Pediatrics, College of Medicine, Soon Chun Hyang University, Seoul, Korea

Abstract

The Prune belly syndrome is a rare congenital anomaly characterized by lax, wrinkled abdominal wall, cryptorchidism and urinary tract anomalies. But it has a wide spectrum of clinical presentation and combine with other anomalies such as pulmonary, skeletal, digestive, cardiovascular and other system. We experienced a case of prune-belly syndrome associated with Turner syndrome in a 18 month old female child.

Keywords :Prune belly syndrome, Turner syndrome