All issues > Volume 36(4); 1993

Case Report

J Korean Pediatr Soc. 1993;36(4):583-588. Published online April 15, 1993.

A Case of VATER Syndrome

Seong Jin SJ Ha¹, Ki Hyun KH Chung¹, Oh Kyung OK Lee¹, Wan Seob WS Kim¹, Jae Seung JS Yang²

¹Department of Pediatrics, Presbyterian Medical Center, Chon Ju, Korea
²Department of Anatomical Pathology, Presbyterian Medical Center, Chon Ju, Korea

Abstract

The VATER syndrome is a group of congenital anomalies with a nonrandom tendency for concurrence. Defects include vertebral, anorectal malformation, tracheoesophageal fisutla with esophageal atresia, radial-limb, vascular, and renal abnormalities. The critical period of organogenesis is at or before the sixth or seventh week of gestation. We experienced one case of VATER syndrome in a 1 day old male neonate having vertebral anomalies, esophageal atresia with tracheoesophageal fistula to the distal esophageal segment, imperforated anus, left renal dysplasia with hydronephrosis of the right kidney and both hydroureter, patent ductus arteriosus. We report a case of VATER syndrome with brief review of related literature.

Keywords :VATER syndrome