All issues > Volume 36(6); 1993

Case Report

J Korean Pediatr Soc. 1993;36(6):865-869. Published online June 15, 1993.

Two Case of Dyke-Davidoff-Masson Syndrome

Dong Gun DG Park¹, Ji Hee JH Park¹, Kee Hwan KH Yoo¹, Ji Tae JT Choung¹, Chang Sung CS Son¹, Young Chang YC Tockgo¹

¹Department of Pediatrics, College of Medicine, Korea University, Seoul, Korea

Abstract

Dyke-Davidoff Masson syndrome is a rare disorder which developed hemiatrophy of brain, enlargement of ventricles and prominet pneumatrization of pertous pyramid of the temporal bone. It manifests hemiparesis, varying type seizure, and mental retardation. We experienced two cases of Dyke-Davidoff-Masson Syndrome, in a 6/12 year-old boy and a 1,10/12 year-old girl who were admitted to our department of pediatrics, because of convulsion and hemiparesis The brain CT sean showed marked dilatation of lateral ventricle, prominent sylvian fissure and cortical sulci. So we report two cases of Dyke-Davidoff-Masson syndrome with review of lierature.

Keywords :Cerebral hemiatrophy, Hemiparesis