All issues > Volume 37(3); 1994

Case Report

J Korean Pediatr Soc. 1994;37(3):410-415. Published online March 15, 1994.

A Case of Rotor Syndrome

Jin Nyoung JN Park¹, In Joon IJ Seol¹

¹Department of Pediatrics, College of Medicine, Hanyang University, Seoul, Korea

Abstract

We experienced a case of Rotor syndrome in an 8 year 6 month old boy who presented with icteric sclera and icteric skin on whole body. His clinical and laboratory characteristics were as follows; 1) Jaundice appeared from several months ago before admission without any clinical disturbance. 2) Direct bilirubin was more increased than indirect bilirubin. 3) Plasma indocyanine green (ICG) kinetics test revealed hepatic excretory defect in this patient that after intravenous injection of a standard dose of ICG (0.5 mg/kg), its initial plasma disappearance is decreased, resulting in markedly increased retention of the dye 45 to 50 minutes after administration. 4) Oral cholangiography, ultrasonogram, and computed tomogram of abdomen were normal. 5) Liver biopsy specimen showed no dark brown pigmentations in the hepatic cells and any other pathologic abnormalities. 6) Nearly similar clinical and laboratory findings were observed 26 months later.

Keywords :Rotor Syndrome