All issues > Volume 37(4); 1994

Case Report

J Korean Pediatr Soc. 1994;37(4):547-552. Published online April 15, 1994.

A Case of Hydranencephaly Combined with Twin Pregnancy

Hong Ju HJ Choi¹, Jin Kil JK Park¹, Hee Tag HT Lim¹, Jae Sam JS Kim¹, Hyo Kyung HK Sin¹, Chul Hoi CH Gu¹, Son Young SY Lee²

¹Department of Pediatrics, Pusan Adventist Hospital, Pusan, Korea
²Department of Radiology, Pusan Adventist Hospital, Pusan, Korea

Abstract

Hydranencehaly is an abnormality consisting of complete or almost absence of the cerebral hemispheres, which are replaced by a large fluid-filled cavity. The midbrain and brain stem are relatively intact, and rudiments of frontal, temporal and occipital cortex may be present. We diagnosed it through the evaluation of clinical features, prenatal US (intrauterine pregnancy, 37 wks) and brain CT. Authors have experienced a case of hydranencephaly combined with twin pregnancy and reported with a brief literature review.

Keywords :Hydranencephaly