All issues > Volume 37(8); 1994

Case Report

J Korean Pediatr Soc. 1994;37(8):1169-1174. Published online August 15, 1994.

A Case of Currino Triad

S.S. SS Park¹, G.H. GH Lee¹, H.S. HS Kim¹, K.H. KH Kim¹, H.S. HS Lee¹, Y.S. YS Lee²

¹Department of Pediatrics, Chung Ang Gil hospital, Incheon, Korea
²Department of Radiology, Chung Ang Gil hospital, Incheon, Korea

Abstract

Currarino triad is a unique malformation complex of congenital caudal anormalies, including anorectal malformation (anal stenosis, anal ectopia, imperforated anus), sacral bony abnormality (scimitar or crescentic bony defect, malsegmentation) and presacral mass (meningocele, teratoma, enteric cyst or any combination of these). This triad is familial in at least half of cases and the usual symptomatology is constipation due to anorectal stenosis. The embryogenesis is presumably due to abnormal separation of the neuroectoderm from the endoderm, so this triad is in the spectrum of the split notochord syndrome. We report a case of Currarino triad in 5-month-old female patient who had chronic constipation and abdominal distention with brief review of the related literatures.

Keywords :Currarino triad