All issues > Volume 37(9); 1994

Case Report

J Korean Pediatr Soc. 1994;37(9):1292-1295. Published online September 15, 1994.

A Case of Miescher Syndrome with Insulin-Resistant Diabetes Mellitus

Byung Min BM Choi¹, Jong Kwang JK Lee¹, Kee Hwan KH Yoo¹, Joo Won JW Lee¹, Soon Kyum SK Kim¹

¹Department of Pediatrics, College of Medicine, Korea University, Seoul, Korea

Abstract

Miescher syndrome comprises congenital acanthosis nigricans, hypertrichosis, failure to thrive and short stature, dysmorphism especially of the jaws and oral cavity. Insulin-resistant diabetes mellitus, and a characteristic general appearance. This report concerns a rare case of 12-year-old girl having insulin resistant diabetic mellitus with Miescher syndrome. The relevant literature was reviewed.

Keywords :Miescher syndrome, Insulin-resistant diabetes mellitus