All issues > Volume 37(10); 1994

Case Report

J Korean Pediatr Soc. 1994;37(10):1463-1469. Published online October 15, 1994.

Two Cases of Total Colon Aganglionosis Involving Small Bowel in Triplet

Won A WA Park¹, Hyun Joo HJ Kim¹, Kyung Dug KD Moon¹, Hea Kyoung HK Lee¹, Young Hee YH Yu¹, Hyun Suk HS Lee¹

¹Department of Pediatrics,Korea Veterans Hospital, Seoul ,Korea

Abstract

Total or mostly total intestinal aganglionosis is rare and invariably fatal. All patients with aganglionosis involving more than half of the small bowel have died with persistent intestinal obstruction and secondary maluntrition and infection. Recently, we experienced two cases of total colon aganglionosis extending to the middle of the jejunum in triplet. We report the cases with brief review of literatures.

Keywords :Total colon aganglionosis, Small bowel