All issues > Volume 38(4); 1995

Case Report

J Korean Pediatr Soc. 1995;38(4):561-566. Published online April 15, 1995.

A Case of Hemimegalencephaly with Intraventricular Hemorrhage and Multifocal Intraparenchymal Hemorrage on Deep White Matter of Periventricular Area

Jin Sung JS Ko², Kook In KI Park², Min Soo MS Park², Moon Sung MS Park², Ran R Namgung², Chul C Lee², Dong Gwang DG Han², Choon Sik CS Yoon¹

¹Department of Diagnostic Radiology, Yonsei University College of Medicine, seoul, Korea
²Department of Pediatrics, Yonsei University College of Medicine, seoul, Korea

Abstract

Hemimegalencephaly is a rare congenital anomaly characterized by a intractable seizure an infantile death. This disease is a migrational disorder with enlargement of unilateral hemisphere, abnormal gyration of the cortex, the presence of large and atypical neuron, hetero trophic neuron at subcortical area and proliferation of astrocyte ect. We observed a neonate with neonatal seizure, and the radiological evaluation revealed abnormal enlargement of right hemisphere, intraventricular hemorrhage of both ventricle and multifocal intraparenchymal hemorrhage on deep white matter of periventricular area on both sides. We used the phenobarbital for treatment of seizure. After phenobarbital treatment. The seizure was controlled. A review of literature was also presented briefly

Keywords :Hemimegalencephaly, Neonate