All issues > Volume 38(10); 1995

Original Article

J Korean Pediatr Soc. 1995;38(10):1349-1355. Published online October 15, 1995.

A Clinical Study of Interrupted Aortic Arch

Myoung Dong MD Shin¹, Tae Hun TH Kang¹, Hyoung Doo HD Lee¹, Si Chan SC Sung²

¹Department of Pediatrics, Dong-A University, College of Medicine, Pusan
²Department of Thoracic & Cardiovascular Surgery, Dong-A University, College of Medicine, Pusan

Abstract

Purpose
: We conducted this study to determine the clinical manifestations and prognostic factors of interrupted aortic arch(IAA).
Methods
: We performed retrospective clinical study with chart review in 9 infants who were diagnosed as IAA between January, 1993 and December, 1994.
Results
: Infants with IA were from 7 days to 92 days of age. Among them, 6 cases were type A, 3 cases were type B. PDA and VSD were seen in all infants with IAA and 2 cases of type B IAA were associated with Taussing-Bing anomaly. For the diagnostic method, 7 infants could be confirmed by echocardiography, so it seems to be relatively accurated diagnostic procedure. We tried PGE,1 in 6 patients with obvious clinical improvement. One of them, even in 53 days old case, there was responsed to PGE1. We attempted complete repair in 6 cases of IAA, 3 patients survived but one patient developed coarctation at anastomosis site, for which we performed balloon angioplasty successfully. With regard to survival rate of patients, for the cases who were diagnosed before 14 days old was 100%, but for the cases who were diagnosed after 14 days since birth, none survived.
Conclusion
: The survival rate in patients of IAA, depends mainly on early recognition and aggressive medical treatment before development of serious symptoms such as cardiogenic shock.

Keywords :Interrupted aortic arch, Balloon angioplasty