All issues > Volume 38(11); 1995

Case Report

J Korean Pediatr Soc. 1995;38(11):1565-1570. Published online November 15, 1995.

A Case of Renal Hypoplasia with Renovascular Hypertension

Sang Doo SD Lee¹, Jae Hee JH Park¹, Jae Beom JB Lee¹, Yun Duk YD Yoo¹, Byoung Hwa BH Lee¹, Mi Sun MS Lee²

¹Department of Pediatrics, Sun General Hospital, Daejeon, Korea
²Department of of Pathology, Sun General Hospital, Daejeon, Korea

Abstract

Renal hypoplasia is a condition in which the kidneys are small because of developmental parenchymal deficit. Essential to this definition is the notion of normally developed and differentiated individual nephrons and ducts, without coexisting dysplasia. Affected renal artery and intrarenal blood vessel branches are relatively hypoplastic and commonly sclerotic. Stenosis of main arteries or its branches are apt to cause hypertension. The pathogenesis of hypoplastic kidneys may involve a diminished number of nephrons and diminished nephrotic size. We experienced a 4-year-old boy with 180/130mmHg of blood pressure, and confirmed renovascular hypertension due to a typical unilateral renal hypoplasia. Nephrectomy was done and the blood pressure returned to normal. Abdominal ultrasonogram, CT, aortic angiography, and pathologic findings are presented with a brief review

Keywords :Renal hypoplasia, Renovascular hypertension, Nephrectomy