All issues > Volume 39(2); 1996

Case Report

J Korean Pediatr Soc. 1996;39(2):273-279. Published online February 15, 1996.

Four Cases of Congenital Esophageal Stenosis Due to Tracheobronchial Remnants

Gi Woong GW Sung¹, So Young SY Lee¹, Yeon Ho YH Choi¹, Kyoung Mo KM Kim¹, Jeong Kee JK Seo¹, In Won IW Kim², Kwi Won KW Park³, Jong Je JJ Kim⁴

¹Department of Pediatrics, College of Medicine, Seoul National University, Seoul, Korea
²Department of Diagnostic Radiology, College of Medicine, Seoul National University, Seoul, Korea
³Department of Pediatric Surgery, College of Medicine, Seoul National University, Seoul, Korea
⁴Department of Pathology, College of Medicine, Seoul National University, Seoul, Korea

Abstract

Esophageal stenosis due to tracheobronchial remnants is a rare cause of congenital esophageal stenosis. The cause is thought to be esophageal sequestration of tracheobronchial remnants during embryonic separation. Errors in diagnosis are common and high index of suspicion is required for accurate diagnosis, and resection of primary site with anastomosis is recommanded. Although a rare entity, esophageal stenosis due to tracheobronchial remnants should be considered in patients with esophageal stenosis, when esophageal stenosis fails to respond to standard therapy including bougienage and balloon dilatation, and esophagoscopy shows normal mucosa on the stenotic segment. Four cases of congenital esophageal stenosis due to tracheobronchial remnants were reported, the first case without accompanied anomaly, the second case accompanied by tracheoesophageal fistula, the third case accompanied by Down syndrome, and the last case accompanied by tracheoesophageal fistula and congenital heart disease.

Keywords :Tracheobronchial remnants, Congenital esophageal stenosis, Esophagoscopy, Tracheo esophageal fistula