All issues > Volume 39(12); 1996

Case Report

J Korean Pediatr Soc. 1996;39(12):1759-1762. Published online December 15, 1996.

An Autopsy Case of Tracheal Agenesis Type 2

Hyun Joo HJ Lee¹, Eun Ae EA Park¹, Seung Joo SJ Lee¹, Mi Jeong MJ Kim², Soon Hee SH Seong²

¹Department of Pediatrics, College of Medicin, Ewha Womans University, Seoul, Korea
²Department of Pathology, College of Medicin, Ewha Womans University, Seoul, Korea

Abstract

Tracheal agenesis is the rare and uniformly lethal anomaly that presents with severe respiratory distress and aphonia after birth. In this anomaly, the trachea is usually absent and air is reaching the bronchi through a communication with the esophagus. The diagnosis should be suspected in a nowborn infant with respiratory distress whose intubation is difficult. We report an autopy case of tracheal agenesis, type 2 in a female newborn infant: Complete tracheal agenesis with the fistula between the esophagus and the carina. Associated anomalies were bilobed right lung, Meckel's divericulum and ventricular septal defect.

Keywords :Respiratory distress, Bronchoesophageal fistula, Tracheal agenesis