All issues > Volume 40(2); 1997

Case Report

J Korean Pediatr Soc. 1997;40(2):270-273. Published online February 15, 1997.

A Case of Neurofibromatosis with Multiple Neurofibromas on Mesentery

Pil Geung PG Hwang¹, Sun Young SY Park¹, Tae Gyu TG Whang¹, Soon Yong SY Lee¹

¹Department of Pediatrics, College of Medicine, Inje University Pusan Paik Hospital, Pusan, Korea

Abstract

Neurofibromatos is originally described by von-Recklinhausen in 1882, is often depicted as a chronic progressive hereditary disease characterized by pigmentation of the skin, cutaneus lesions, and numerous tumors developing in association with elements of both the central and peripheral nervous tissue. Mesenteric involvements in neurofibromatosis are very rare in childrens. We experienced a case of neurofibromatosis with multiple neurofibromas on mesentery in 6 years old male who presented with abdominal pain. The diagnosis was confirmed by clinical manifestations, abdominal CT, and histopathologic findings. Brief review of literatures was made.

Keywords :Neurofibromatosis, Neurofibromas, Mesentery