All issues > Volume 40(4); 1997

Case Report

J Korean Pediatr Soc. 1997;40(4):567-571. Published online April 15, 1997.

One Case of Congenital Complete Atrioventricular Block Diagnosed by Fetal Echocardiography

Eun Jung EJ Kim¹, Tae Hoon TH Kang¹, Hyoung Doo HD Lee¹

¹Department of Pediatrics, Dong-A University College of Medicine, Pusan, Korea

Abstract

Congenital complete atrioventicular block is uncommon which has a heterogenous etiology. According to recent studies, about one-third of the mothers of the patients who were diagnosed as congenital complete atrioventricular block, had symptoms or signs of connective tissue disease. Even though the outlook is usually regarded as favorable, the mortality is highest in the neonatal period, much lower during childhood and adolescence and increases slowly later in life. In the neonatal period the predominant indication for pacing was heart failure. It is difficult to make a prognosis in the individual patient. A slow, fixed or decreasing venticular rate neonatally and a prolonged QT interval seem to be bad prognostic sign. We report a case of congenital complete atrioventricular block who was diagnosed by fetal echocardiography. Her mother was asymptomatic, but had positive serologic test to anti-Ro antibody and anti-La antibody. We report a case of congenital complete atrioventricular block with a brief review of related literatures.

Keywords :Congenital complete atrioventricular block, Fetal echocardiography, Connective tissue disease