All issues > Volume 41(11); 1998

Case Report

J Korean Pediatr Soc. 1998;41(11):1601-1605. Published online November 15, 1998.

A Case of Myositis Ossificans Progressiva

So Young SY Park¹, Su Jin SJ Lee¹, Ji A JA Chung¹, Seung Joo SJ Lee¹

¹Department of Pediatrics, College of Medicine, Ewha Womans University, Seoul, Korea

Correspondence So Young SY Park ,Email: 1

Abstract

Myositis ossificans progressiva(MOP) is a rare, slow progressive autosomal dominant disorder that principally affects children under the age 10 years. It is characterized by progressive fibroblastic proliferation, and subsequent calcification and ossification of subcutaneous fat, muscles, tendons, aponeuroses and ligaments. The disorder is often associated with symmetrical malformations of the digits, especially microdactyly or adactyly of the thumbs and great toes. The disease usually leads to extensive immobility and eventual disability. We experienced a case of MOP in a 2-year-old male child who showed multiple tender nodules on the left occipital, superior and inferior scapular, mid-back and upper buttock area and digital malformations and was treated with etidronate disodium. A brief review of related literatures is also presented.

Keywords :Myositis ossificans progressiva, Digital malformations