All issues > Volume 42(4); 1999

Original Article

J Korean Pediatr Soc. 1999;42(4):535-544. Published online April 15, 1999.

Congenital Esophageal Stenosis : with Special Reference to Diagnosis and Postoperative Complications

Ju Young JY Jang¹, Jae Seong JS Ko¹, Kwi Won KW Park², Woo Seon WS Kim³, In Won IW Kim³, Ja Jun JJ Jang⁴, Jeong Kee JK Seo,¹

¹Department of Pediatrics, Seoul National University College of Medicine, Seoul, Korea
²Department of Surgery, Seoul National University College of Medicine, Seoul, Korea
³Department of Radiology, Seoul National University College of Medicine, Seoul, Korea
⁴Department of Pathology, Seoul National University College of Medicine, Seoul, Korea

Correspondence Jeong Kee JK Seo, ,Email: 1

Abstract

Purpose
: Congenital esophageal stenosis(CES) is one of the rare causes of recurrent vomiting during infancy and childhood. We studied the diagnostic and therapeutic tools and postoperative complications for early diagnosis and adequate management of CES.
Methods
: Fourteen cases of CES were evaluated for clinical manifestations, findings of esophagogram and esophagoscopy, classification of pathologic findings and postoperative complications.
Results
: Most common clinical manifestations at onset were non-projectile vomiting(14), dysphagia to solids(13). Age at onset of symptoms corresponded with the introduction of solids in 11 cases. Esophagogram showed segmental stenosis of variable length in the lower portion of the esophagus in all cases with marked proximal dilatation in 11 cases. Esophagoscopy revealed no signs of esophagitis or ulcer at the area of stenosis. Segmental resection and primary anastomosis were performed as a definitive treatment modality in all cases except one with fibromuscular stenosis. Bronchial cartilage were present in all cases of tracheobronchial remnants(10). Abnormal arrangement and thickening of muscularis mucosae and inner circular muscle were found in all cases of fibromuscular stenosis(4). Postoperative complications were gastroesophageal reflux(5), stricture of anastomotic sites, reflux esophagitis, and so on.
Conclusion
: CES is rare but should be considered as a cause of recurrent vomiting and dysphagia to solid food beginning in infancy and childhood especially in the weaning period. Esophagogram and esophagoscopy are useful tools for diagnosis and differential diagnosis. The stricture of anastomosis site, gastroesophageal reflux and esophagitis need to be evaluated in the follow-up postoperative periods.

Keywords :Congenital esophageal stenosis, Dysphagia, Tracheobronchial remnants, Idiopathic fibromuscular stenosis