All issues > Volume 43(5); 2000

Case Report

J Korean Pediatr Soc. 2000;43(5):715-719. Published online May 15, 2000.

A Case of Fibromuscular Dysplasia Associated with Hypertensive Encephalopathy

Ju Suk JS Lee¹, Sang Nam SN Bae¹, Sang Ook SO Nam¹, Su Young SY Kim¹, Hee Ju HJ Park¹

¹Department of Pediatrics, College of Medicine, Pusan National University, Pusan, Korea

Abstract

Fibromuscular dysplasia is the single leading etiology of renovascular hypertension in children. We report an eight-year-old girl who was admitted for generalized tonic seizure with fibromuscular dysplasia of right renal artery. On admission, she presented hypertension and altered mentality. She had suffered from intermittent severe headache for the past year. Renal angiography of right renal artery showed stenosis, beaded pattern and aneurysms. Brain MRI showed multifocal lesions in parietooccipital, periventricular and external capsular area. She was diagnosed as hypertensive encephalopathy due to fibromuscular dysplasia of renal the artery. Renal angioplasty with ballooning catheter was performed. Successful renal angioplasty dropped her blood pressure to normal level and no more headaches has occurred for more than a year after discharge.

Keywords :Fibromuscular dysplasia, Hypertensive encephalopathy