All issues > Volume 43(8); 2000

Case Report

J Korean Pediatr Soc. 2000;43(8):1122-1126. Published online August 15, 2000.

Two Cases of Left Ventricular Tumors Complicating Subaortic Stenosis in Newborn Infants

Ji Seon JS Kang¹, Mi Jung MJ Hwang¹, Tae Hyoung TH Cho¹, Byung Ju BJ Kim¹, Young Jong YJ Woo¹, Jae Sook JS Ma¹

¹Department of Pediatrics, Chonnam National University Medical School, Kwangju, Korea

Abstract

The most common obstruction of left ventricular outflow in childhood is produced either by a fibrous ring below the aortic valve, or by localized or diffuse muscular hypertrophy of the interventricular septum. Cardiac tumors causing subaortic stenosis in the newborn infant are extremely rare. This report describes two cases of subaortic stenosis caused by a tumor of the left ventricle in newborn infants, both diagnosed by 2-dimensional echocardiography. In one patient, the obstructive portion of the tumor was successfully resected from its attachment to the ventricular septum by aortotomy on day 5. Histologic examination confirmed the diagnosis of rhabdomyoma. This patient developed cutaneous, neurologic and radiologic abnormalities of tuberous sclerosis during the follow-up of 42 months.

Keywords :Heart, Rhabdomyoma, Subaortic stenosis, Tuberous sclerosis