All issues > Volume 43(11); 2000

Original Article

J Korean Pediatr Soc. 2000;43(11):1458-1464. Published online November 15, 2000.

Study of Congenital Mitral Stenosis Cases Requiring Surgical Correction in the First 2-Years of Life

In Seung IS Park¹, Young Seok YS Lee¹, Mi Young MY Han¹, Jae Young JY Lee¹, Soo Jin SJ Kim¹, Do Jun DJ Cho¹, Mee-Hye MH Oh², Woong-Han WH Kim³, Young-Tak YT Lee³, Eun Jung EJ Bae⁴, Seong Ho SH Kim⁵

¹Department of Pediatrics, Sejong General Hospital, Pucheon, Korea
²Department of Pathology, Sejong General Hospital, Pucheon, Korea
³Department of Surgery, Sejong General Hospital, Pucheon, Korea
³Department of Surgery, Sejong General Hospital, Pucheon, Korea
⁴Department of Pediatrics, Seoul National University, College of Medicine, Seoul, Korea
⁵Department of Pediatrics, Gachon Medical University, Incheon, Korea

Abstract

Purpose
: Congenital mitral stenosis(CMS) is a rare anomaly accounting for 0.4-0.5% of total heart disease. CMS which cases needed surgical correction in infancy are even rare. In this study, we analyzed 11 CMS patients of less than 2 year of age who needed surgical corrections, in order to find out their diagnoses, the characteristics, the results of operation and prognoses, and the progress of disease without surgical correction.
Methods
: Retrospective studies were performed on eleven CMS patients of less than 2 years of age admitted to Sejong General Hospital between Jan. 1989 and Aug. 1999.
Results
: The surgeries were performed on 9 out of 11 enrolled patients. The median age was 8(3-20) months and the median weight was 5(4-9)kg. The mitral valves of the patients were classified anatomically as supramitral ring(4), parachute mitral valve(3), “typical” symmetric hypoplastic mitral valve(2) and asymmetric hypoplastic mitral valve(2). Three patients died after the surgical correction. Among them, fibroelastosis of left ventricle was found during the surgery in two cases, and the other case was considered to be in Eisenmenger state. 5. Reoperations were performed on 3 out of 6 surviving patients. While one case was an early reoperation, two cases were late ones.
Conclusion
: The patients with severe CMS under the age of two can be surgically corrected with an acceptable success rate. Poor results were observed, however, if the decisions for surgical intervention were delayed.

Keywords :Congenital mitral stenosis