All issues > Volume 44(1); 2001

Case Report

J Korean Pediatr Soc. 2001;44(1):89-93. Published online January 15, 2001.

A Case of Distal Renal Tubular Acidosis Associated with Medullary Sponge Kidney

Sung Jun SJ Jang¹, Jo Yun JY Jung¹, Jun Sik JS Kim¹, Heung Sik HS Kim¹, Hee Jung HJ Lee²

¹Department of Pediatrics, School of Medicine, Keimyung University, Daegu, Korea
²Department of Diagnostic Radiology, Keimyung University, Daegu, Korea

Abstract

Renal tubular acidosis is a clinical state of systemic hyperchloremic acidosis resulting from impaired urine acidification. Medullary sponge kidney is a renal parenchymal malformation characterized by cystic dilatation of the collecting ducts. Although medullary sponge kidney is a congenital disease, it is rarely identified in childhood and is usually discovered in adulthood. Medullary sponge kidney patients may have defects in urinary acidification and concentration mechanism. We experienced a case of distal renal tubular acidosis associated with medullary sponge kidney. So, we report a case of distal renal tubular acidosis associated with medullary sponge kidney with a brief review of the related literature.

Keywords :Medullary sponge kidney, Distal renal tubular acidosis