All issues > Volume 44(1); 2001

Case Report

J Korean Pediatr Soc. 2001;44(1):99-102. Published online January 15, 2001.

A Case of Congenital Nasal Pyriform Aperture Stenosis

Hyoung Sik HS Oh¹, Sang Hee SH Kim¹, Gil Hyun GH Kim¹, Hak Soo HS Lee¹, Il Hwan IH Jang², Ji Hae JH Kim³

¹Department of Pediatrics, Gachon Medical School, Incheon, Korea
²Department of Otolaryngology, Gachon Medical School, Incheon, Korea
³Department of Diagnostic Radiology, Gachon Medical School, Incheon, Korea

Abstract

The cause of congenital nasal pyriform aperture stenosis is unclear. The development of the facial skeleton occurs between the fifth and the eighth week of gestation. It is at this stage that the stenosis occurs due to overgrowth of the ossification of the maxilla. Infants are obligate nasal breathers. Incomplete and milder forms of nasal airway obstruction may be present with mild respiratory distress, cyanosis, respiratory failure, asphyxia and eventual death. The diagnosis is done by CT, which demonstrates marked narrowing of the nasal inlet. Mild stenosis can be managed conservatively with humidification and topical decongestants but if conservative treatment fails, surgical intervention is candidate. We report a case of congenital nasal pyriform aperture stenosis. The patient, a 2-day old male neonate, had cyanosis during feeding and noisy breathing relieved by crying. His symptoms and signs were improved with surgical intervention without development disturbances.

Keywords :Congenital nasal pyriform aperture stenosis, Respiratory distress, Cyanosis