All issues > Volume 44(11); 2001

Case Report

J Korean Pediatr Soc. 2001;44(11):1326-1329. Published online November 15, 2001.

A Case of Disseminated Lymphangiomatosis Involving Mediastinum, Bone, Spleen and Retroperitoneum in an Asymptomatic Healthy Child

Kyung Hee KH Yoon¹, Seung Ju SJ Ha¹, In Sook IS Park¹, Hyun Woo HW Goo², Jong Hyun JH Yoon²

¹Department of Pediatrics, College of Medicine, Ulsan University, Seoul, Korea
²Department of Diagnostic Radiology, College of Medicine, Ulsan University, Seoul, Korea

Correspondence In Sook IS Park ,Email: ispark@amc.seoul.kr

Abstract

Lymphangiomatosis, a benign tumor consisting of a cluster of dilated lymphatic channels, is very unusual. Most lymphangiomatoses are found in the neck and head area. Less than 5% are diagnosed intraabdominally and they are very infrequently encountered in the retroperitoneal area. Herein, we report a rare case of asymptomatic lymphangiomatosis of a 13 year-old boy during a routine chest radiologic exam at school who had disseminated lymphangiomatosis involving anterior mediastinum, multiple bone, spleen and retroperitoneum, which presented occasionally.

Keywords :Lymphangiomatosis, Mediastinum, Bone, Spleen, Retroperitoneum