All issues > Volume 45(10); 2002

Case Report

J Korean Pediatr Soc. 2002;45(10):1292-1297. Published online October 15, 2002.

A Case of Melkersson-Rosenthal Syndrome

Dae Hun DH Pee¹, Yo Won YW Na¹, Ki Young KY Chang¹, Woo Keun WK Seo², Kee Hyoung KH Lee¹, Baik-Lin BL Eun¹

¹Department of Pediatrics, College of Medicine, Korea University, Seoul, Korea
²Department of Neurology, College of Medicine, Korea University, Seoul, Korea

Correspondence Baik-Lin BL Eun ,Email: bleun@chollian.net

Abstract

Melkersson-Rosenthal syndrome(MRS) is a rare disorder, having a symptom triad of recurrent facial palsy, orofacial swelling and fissured tongue(lingua plicata). This disorder is usually recurrent or progressive, and monosymptomatic or oligosymptomatic forms have been reported to be more common than classic forms. Generally, MRS occurs in young adults at the end of the second decade of life and incidence of the disease in childhood is known to be very low. Although the clinical manifestation of MRS in children is similar to that in adults, early diagnosis and management is essential to avoid long-lasting functional disorders and psychological problems. We experienced MRS in a 13 year old boy with a history of recurrent facial palsy. We report this case with review of related literature.

Keywords :Melkersson-Rosenthal Syndrome