All issues > Volume 45(10); 2002

Case Report

J Korean Pediatr Soc. 2002;45(10):1292-1297. Published online October 15, 2002.

A Case of Systemic Capillary Leak Syndrome in a Child

Taeg Young TY Lee¹, Yoo Mi YM Chung¹, Hee Gyung HG Kang¹, Il Soo IS Ha¹, Hae Il HI Cheong¹, Yong Y Choi¹

¹Department of Pediatrics, Seoul National University College of Medicine, Seoul, Korea

Correspondence Il Soo IS Ha ,Email: ilsooha@snu.ac.kr

Abstract

Systemic capillary leak syndrome(SCLS) is a rare disorder of unknown etiology, which is characterized by recurrent attacks of hypotension, hemoconcentration, and hypoalbuminemia. Urinary or enteric loss of protein is not demonstrated. It is often associated with monoclonal gammopathy, but does not manifest multiple myeloma. Since Clarkson et al. described the first case in a 34- year-old woman, about 50 cases have been reported in the literature. However, most of the cases were of adult age, and the mean age of onset in the reported cases was 42.6 years. In literature review, we could refer only one pediatric case of SCLC by Foeldvari et al. in 1995. We report another pediatric case of SCLS.

Keywords :Systemic capillary leak syndrome, Child