All issues > Volume 47(2); 2004

Case Report

Korean J Pediatr. 2004;47(2):214-216. Published online February 15, 2004.

A Case of Systemic Sclerosis in a Child

Ji Yeon JY Chang¹, Ja Kyoung JK Kim¹, Jeong Hee JH Kim¹, Dae Hyun DH Lim¹, Byong Kwan BK Son¹, Jung Soo JS Song²

¹Department of Pediatrics, College of Medicine, Inha University, Incheon, Korea
²Department of Internal Medicine, College of Medicine, Inha University, Incheon, Korea

Abstract

Systemic sclerosis is a connective tissue disease involving primarily the skin and subcutaneous tissue but may involve other organ systems such as the lungs, gastrointestinal tract, and heart. Systemic sclerosis is a rare childhood disease. The age of onset for patients with systemic sclerosis has its peak between 30 and 50 years of age. Only 1 to 2% of all patients with systemic sclerosis have disease onset before the age of 10 years of age. We report a case of systemic sclerosis in a 7- year-old female who showed Raynaud's phenomenon as an initial manifestation.

Keywords :Raynaud's phenomenon, Systemic sclerosis