All issues > Volume 47(8); 2004

Case Report

Korean J Pediatr. 2004;47(8):908-911. Published online August 15, 2004.

A Case of Biliary Atresia with Ileal Atresia

So Yeon SY Kim¹, Hyun Jung HJ Na¹, Woo Taek WT Kim¹, Woo Hyun WH Park², Jin Kyung JK Kim¹

¹Department of Pediatrics, College of Medicine, The Catholic University of Korea
²Department of General Surgery, College of Medicine, Keimyung University, Daegu, Korea

Correspondence Jin Kyung JK Kim ,Email: kimjk@cu.ac.kr

Abstract

Biliary atresia is a progressive obliterative cholangiopathy. However, the actual causes remain unknown, although a number of factors such as developmental malformation, viral infection, toxicity of bile constituents, and anatomic abnormality in the hepatobiliary system have been considered. Recently, several studies have been done to find out specific gene expression. Some cases of biliary atresia are associated with anomalies of cardiovascular system, digestive tract and spleen. Few cases of biliary atresia with congenital ileal atresia were reported. We experienced a case with biliary atresia combined with ileal atresia. Ileal resection and end to end anastomosis operation were done at second days of the life because of congenital ileal atresia. Jaundice and acholic stool were noticed a few days after the operation. He was diagnosed as biliary atresia and received Kasai operation at 23 days of the life. Therefore, we report the case with a brief review of the related literature.

Keywords :Biliary, Ileal, Atresia