All issues > Volume 47(12); 2004

Case Report

Korean J Pediatr. 2004;47(12):1334-1337. Published online December 15, 2004.

Melanotic Neuroectodermal Tumor of Infancy in the Epididymis : A Case Report

Sang Bae SB Lee¹, Seong Hun SH Lee¹, Min Hyuk MH Ryu¹, Ji Seoung JS Park², Joo Heoun JH Yang², Sun Young SY Kim¹, Dong Jean DJ Lee¹

¹Department of Pediatrics, Urology* and Pathology†, Dong Kang General Hospital, Ulsan, Korea
²Department of Pediatrics, Urology* and Pathology†, Dong Kang General Hospital, Ulsan, Korea

Correspondence Dong Jean DJ Lee ,Email: djleekr@hanmail.net

Abstract

Melanotic neuroectodermal tumor of infancy (MNTI) is a rare neoplasm known by a variety of names including melanotic progonoma and retinal anlage tumor, and currently thought to be neural crest derivation. The vast majority develop within the first year of life. The behavior is generally benign, but recurrent and metastatic cases have been documented. It arises in the head and neck in over 90%, mainly in the maxilla, but is extremely rare in the epididymis. We report a case of MNTI together with a review of literature, which occurred in the right epididymis of a 6-month-old boy who presented with a painless, slowly growing, scrotal mass and was treated with radical orchiectomy.

Keywords :Melanotic neuroectodermal tumor of infancy , Epididymis