All issues > Volume 48(1); 2005

Case Report

Korean J Pediatr. 2005;48(1):104-107. Published online January 15, 2005.

A Case of Choledochal Cyst Complicated by Liver Cirrhosis on Pathology in a 20-Month-Old-Girl

Sun Hwan SH Bae¹, Sung Yun SY Choi², Tae Seok TS Lee³, Ho Jeong HJ Lee⁴

¹Department of Pediatrics, School of Medicine, Konkuk University, Seoul, Korea
²Department of Pediatrics, School of Medicine, Eul-Ji University, Seoul, Korea
³Department of General Surgery, School of Medicine, Eul-Ji University, Seoul, Korea
⁴Department of General Surgery, School of Medicine, Eul-Ji University, Seoul, Korea

Correspondence Sun Hwan SH Bae ,Email: baedori@hanafos.com

Abstract

Choledochal cyst is considered to be congenital anomalies of the biliary tract, characterized by varying degrees of cystic dilatation at various segments of the biliary tract. A 20-month-old girl was admitted to Eul-Ji general hospital because of abdominal distension. Physical examination revealed marked splenomegaly and hepatomegaly with nodular surface and hard consistency. Laboratory examination showed elevated transaminase level, alkaline phosphatase level and gamma glutamyltranspeptidase level without evidence of cholestasis. Diagnostic imaging study revealed choledochal cyst with Todani classification type 1. Cholecystectomy and Roux-en-Y choledochojejunostomy was performed, and wedge liver biopsy showed diffuse periportal fibrosis with cirrhotic change and ductular proliferation in the portal area. After operation, hepatosplenomegaly and abnormal laboratory examinations improved rapidly, and in 9 months, the liver and spleen became not palpable. We experienced a case of choledochal cyst complicated by liver cirrhosis on pathology in a 20 month-old girl, and removal of choledochal cyst improved clinical manifestations rapidly.

Keywords :Choledochal cyst, Liver cirrhosis, Child