All issues > Volume 48(2); 2005

Case Report

Korean J Pediatr. 2005;48(2):224-227. Published online February 15, 2005.

A Case of Protein Losing Enteropathy Associated with Henoch-Sch nlein Purpura

Kee Dae KD Kim¹, Chang Whan CW Oh¹, Eun Young EY Lee¹, Jae Young JY Kim¹

¹Department of Pediatrics, St. Benedict Hospital, Busan, Korea

Correspondence Jae Young JY Kim ,Email: jykim9@korea.com

Abstract

Henoch-Sch nlein purpura(HSP) is an IgA mediated immune complex vasculitic disease characterized by non-thrombocytic purpura, arthritis, gastrointestinal manifestations, and glomerulonephritis. HSP related glomerulonephritis induces hypoproteinemia and edema in some cases. Protein-losing enteropathy is another rare but known manifestation of HSP leading to hypoproteinemia and edema. We report a 6-year-old girl with HSP who showed edema caused by intestinal protein loss, evidenced by elevated fecal alpha 1 antitrypsin clearance.

Keywords :Henoch-Sch nlein purpura , Protein losing enteropathy