All issues > Volume 48(2); 2005

Case Report

Korean J Pediatr. 2005;48(2):228-231. Published online February 15, 2005.

A Case of Atypical Teratoid/Rhabdoid Tumor Arising from the Supratentorial Area

Kyeong Hun KH Jung¹, Young Se YS Kwon¹, Yong Hun YH Jun¹, Soon Ki SK Kim¹, Young Jin YJ Hong¹, Byong Kwan BK Son¹, Eun Young EY Kim², In Suh IS Park³

¹Department of Pediatrics, College of Medicine, Inha University, Incheon, Korea
²Department of Neurosurgery, College of Medicine, Inha University, Incheon, Korea
³Department of Pathology, College of Medicine, Inha University, Incheon, Korea

Correspondence Young Se YS Kwon ,Email: ysped@inha.ac.kr

Abstract

Atypical teratoid/rhabdoid tumor may arise at any central nervous system location, but it is most commonly located in the cerebellum(60 percent). The incidence of this tumor remains unclear but it occurs most commonly in children less than 2 years of age. This highly malignant tumor shows a rapid progression and nonspecific radiologic findings. We report a case of primary intracranial atypical teratoid/rhabdoid tumor arising from the supratentorial area in early infancy. The diagnosis was made based on distinctive light microscopy and immunohistochemical findings. Despite aggressive surgical treatment with adjuvant chemotherapy, he died six months after his second operation.

Keywords :Atypical teratoid/rhabdoid tumor , Supratentorium