All issues > Volume 48(11); 2005

Case Report

Korean J Pediatr. 2005;48(11):1256-1259. Published online November 15, 2005.

Intervention with Balloon Valvuloplasty followed by Patent Ductus Arteriosus Stent in a Patient with Pulmonary Atresia with Intact Ventricular Septum

Han Hyuk HH Lim¹, Young Deuk YD Kim¹, Jae Hwan JH Lee¹, Mea Young MY Chang², Hong Ryang HR Kil¹

¹Department of Pediatrics, College of Medicine, Chungnam National University, Daejeon, Korea
²Department of Internal Medicine, College of Medicine, Chungnam National University, Daejeon, Korea

Correspondence Hong Ryang HR Kil ,Email: gilhong@cnu.ac.kr

Abstract

Pulmonary atresia with intact ventricular septum (PAIVS) is rare, less than 1% of congenital heart disease. It needs a therapeutic approach according to its individual morphologic feature. Surgical treatment of valvotomy and modified Blalock-Taussig shunt or non-surgical interventional catheter balloon valvuloplasty can be used for mild to moderate hypoplasia of right ventricle. Fontan operation can be considered for less optimum morphological substrate of two ventricular repair. A 3- day-old male neonate was admitted with cyanosis and cardiac murmur. On echocardiogram, he had membranous pulmonary atresia with intact ventricular septum, normal sized tripartite right ventricle, large atrial septal defect with right-to-left shunt, small sized patent ductus arteriosus, and moderate tricuspid regurgitation. He was treated with intravenous continuous infusion of prostaglandin E1 (PGE1) at once. On the third day of hospitalization, Balloon valvuloplasty was performed. After insertion of patent ductus arteriosus stent on the tenth day, PGE1 infusion was discontinued. On the fifteenth day, he was discharged. Now, he is 9 months old and has nearly normal cardiac structure and function with 97% of percutaneous oxygen saturation.

Keywords :Pulmonary Atresia , Balloon Valvuloplasty , Stent