All issues > Volume 50(3); 2007

Case Report

Korean J Pediatr. 2007;50(3):302-305. Published online March 15, 2007.

A case of adrenocortical adenoma following long-term treatment in a patient with congenital adrenal hyperplasia

Seung Rim SR Lho¹, So Hyun SH Park¹, Min Ho MH Jung¹, Byung Churl BC Lee¹

¹Department of Pediatrics, College of Medicine, The Catholic University of Korea, Seoul, Korea

Correspondence Byung Churl BC Lee ,Email: byungcl@catholic.ac.kr

Abstract

As a result of the widespread use and enhanced quality of high-resolution radiological techniques, a recent report has revealed a relatively high prevalence of small adrenal tumors in patients with untreated congenital adrenal hyperplasia due to 21-hydroxylase deficiency. However, there are scarcely any pediatric cases of adrenocortical tumor following long-term treatment in patients suffering with congenital adrenal hyperplasia. We report here on a pediatric female case of adrenocortical adenoma despite adequate long-term treatment for the salt-losing type of congenital adrenal hyperplasia.

Keywords :Congenital adrenal hyperplasia , Adrenocortical tumor