All issues > Volume 51(1); 2008

Case Report

Korean J Pediatr. 2008;51(1):98-101. Published online January 15, 2008.

Primary leiomyosarcoma of the chest wall in a child : a case report

Jae Hyuk JH Choi¹, David Chanwook DC Chung¹, Mee Jeong MJ Lee¹

¹Department of Pediatrics, Dankook University College of Medicine, Cheonan, Chungnam, Korea

Correspondence Mee Jeong MJ Lee ,Email: LMJPED@dankook.ac.kr

Abstract

Leiomyosarcoma is an uncommon soft tissue sarcoma of mesenchymal cell origin, which shows smooth muscle differentiation. Leiomyosarcoma is seldom found in the pediatric population, and accounts for fewer than 2% of all soft tissue sarcomas. Leiomyosarcoma of the chest wall is extremely rare in children. We report here a case of an 8-year-old boy with a primary leiomyosarcoma that was incidentally found as a rib mass. The patient underwent a complete resection for a suspected osteochondroma diagnosed by a three-dimensional chest computed tomography examination. Pathological findings of the mass revealed intersecting fascicles of spindle cells showing cigar-shaped nuclei, inconspicuous nuclear pleomorphism and occasional mitotic figures in the background of a suspected osteochondroma of the rib. This report documents the first description of a leiomyosarcoma possibly arising in an osteochondroma of the rib in a child.

Keywords :Leiomyosarcoma, Chest wall, Rib, Osteochondroma, Child