All issues > Volume 51(9); 2008

Case Report

Korean J Pediatr. 2008;51(9):1018-1022. Published online September 15, 2008.

A case of testicular adrenal rest tumor in a male child with congenital adrenal hyperplasia

Joo Hwa JH Kim¹, Kyong Ah KA Yun¹, Choong Ho CH Shin¹, Sei Won SW Yang¹

¹Department of Pediatrics, College of Medicine, Seoul National University, Seoul, Korea

Correspondence Choong Ho CH Shin ,Email: chshinpd@snu.ac.kr

Abstract

Testicular adrenal rest tumors are a well-known complication in male patients with congenital adrenal hyperplasia. Corticosteroid suppressive therapy usually results in the regression of these tumors. We describe a patient with 21-hydroxylase deficiency who developed bilateral testicular masses. Despite steroid suppressive therapy, the tumors did not regress and hormonal control was poor. Consequently, bilateral partial orchiectomies were performed.

Keywords :Testicular neoplasms, Adrenal rest tumor, Child, Congenital adrenal hyperplasia, Steroid, 21-hydroxy