All issues > Volume 34(10); 1991

Original Article

J Korean Pediatr Soc. 1991;34(10):1446-1451. Published online October 31, 1991.

A case of incontinentia pigmenti.

Kwang Ik Song¹, Hyo Jeong Kim¹, Jin Bok Hwang¹, Chang Ho Han¹, Hye Li Chung¹, Young Dae Kwon¹

¹Department of Pediatrics, Catholic Hospital, Taegu, Korea

Received: May 7, 1991;  Accepted: July 10, 1991.

Abstract

A case of incontinentia pigmenti, Bloch-Sulzberger type, without any developmental defect has been presented with the review of related literatures. The patient was a 4 day-old female infant with irregular, grouped vesicobullous lesions on the whole body, especially on the trunk and extremities since birth. No familial traits was noted. Diagnosis was made by the charateristic clinical, labaratory and histopathologic findings.

Keywords :Incontinentia Pigmenti;Bloch-Sulzberger type