All issues > Volume 34(10); 1991

Original Article

J Korean Pediatr Soc. 1991;34(10):1373-1380. Published online October 31, 1991.

The clinical review of congenital magacolon.

Myung Goo Min¹, Ki Sup Chung¹

¹Department of Pediatrics, Yonsei University College of Medicine, Seoul, Korea

Received: May 7, 1991;  Accepted: June 24, 1991.

Abstract

This clinical study presents an anlaysis of 102 patients who underwent definitive surgery for Hirschsprung’s disease from January 1979 to April 1990 at Department of Pediatrics, Yonsei Univer- sity College of Medicine. The results were summarized briefly as follows: 1) The sex ratio was 2.6:1, of male preponderence. 2) The first symptom appeared within 1 month after birth in majority of cases, in 82 cases (80.4%) and diagnosis were made under 1 year of age in 66 cases (64.7%). 3) The clinical symptoms were abdominal distension (71.6%), constipation (59.8%), vomiting (33. 3%) in order of frequency, and 41 cases (40.2%) showed delayed in meconium passing. 4) In majority of cases (86.4%), aganglionic segment was located in upper rectum and rectosigmoid so called short segment type and the total aganglinosis was 9 cases (8.8%) among 14 cases of long segment type. 5) The associated anomalies were 9 cases (8.8%), which were inguinal hernia, hydrocele, polydact- ly, megabladder, imperforate anus, intestinal malrotation, ileal stenosis. 6) The pathologic findings show absence of ganglion cells (79.4%), hypoplasia of ganglion cells (5. 9%), decreased number of ganglion cells (7.8%). 7) Of 102 cases, the preliminary colostomy was done in 71 cases and definitive surgery was performed in 69 cases in which 61 cases received DuhameFs procedure. 8) The incidence of postoperative complication of preliminary colostomy was 17.1% and that of definitive operation was 32.3%. 9) The majority of cases (84.3%) improved after operation and the overall mortality rate was 5. 9%. The causes of death were 4 cases of sepsis, 1 case of asphyxia and 1 case of malnutrition.

Keywords :Congenital megacolon;Hirschsprung's disease