All issues > Volume 34(8); 1991

Original Article

J Korean Pediatr Soc. 1991;34(8):1139-1145. Published online August 31, 1991.

Tricuspid atresia associated with double orifice mitral valve and coronary sinus septal defect.

In Sook Park¹, Ki Soo Kim¹, Young Seo Park¹, Chang Yee Hong¹, Shi Joon Yoo², Meong Gun Song³

¹Department of Pediatrics, Asan Medical Center, Ulsan University, Seoul, Korea
²Department of Radiology, Asan Medical Center, Ulsan University, Seoul, Korea
³Department of Thoraic Surgery, Asan Medical Center, Ulsan University, Seoul, Korea

Received: December 28, 1990;  Accepted: March 13, 1991.

Abstract

Clinical, echocardiographic and angiographic findings of a very rare case of cardiac malformation is presented. The main features were tricuspid atresia, coronary sinus septal defect, and double orifice mitral valve. These defects were correctly diagnosed by echocardiography and were confirmed by angiocardiography. This patient was palliated successfully with blade balloon atrial septostomy and bidirectional cavopulmonary shunt. To the best of our knowledge, this is the first reported case of such a combinatin of congenital cardiac malformations in English literature. Also we believe this is the first report of blade atrial septostomy performed in Korea.

Keywords :Tricuspid atresia;Double orifice mitral valve;Coronary sinus septal defect;Blade atrial septostomy;Bidirectional cavo-pulmonary shunt