All issues > Volume 34(6); 1991

Original Article

J Korean Pediatr Soc. 1991;34(6):869-876. Published online June 30, 1991.

A case of myelofibrosis with juvenile xanthogranuloma.

Jong Chan Kim¹, Hae Yong Lee¹, Hwang Min Kim¹, Baek Keun Lim¹, Jong Soo Kim¹, Young Hyuk Lee²

¹Department of Pediatrics, Yonsei University, Wonju College of Medicine, Wonju, Korea.
²Department of Pediatrics, Min Joong HospitaI，Konkuk University, College of Medicine

Received: November 20, 1990;  Accepted: February 26, 1991.

Abstract

Myelofibrrosis is characterized by anemia, leukoerythroblastosis, extramedullary hematopoiesis, hepatosplenomegaly, osteosclerosis and fibrosis of bone marrow. Idiopathc myelofibrosis is usually a disease of the adult and is rare in the pediatric age group. Juvenile xanthogranuloma is characterized by multiple papules on forehead and scalp. Lipid laden histiocytes and Touton giant cell are found in skin biopsy. We experienced a case of myelofibrosis with juvenile xanthogranuloma. So, we presented the case and brief review of literatures.

Keywords :Mylofibrosis;Juvenile xanthogranuloma