All issues > Volume 34(6); 1991

Original Article

J Korean Pediatr Soc. 1991;34(6):779-786. Published online June 30, 1991.

The muscular ventricular septal defect and multiple ventricular septal defects in some congenital heart diseases.

Young Hwi Kim¹, Ki Soo Kim¹, Chung Il Noh¹, Jung Yun Choi¹, Yong Soo Yoon¹, In One Kim², Kyung Mo Yeon²

¹Department of Pediatrics, Seoul National University College of Medicine, Seoul, Korea
²Department of Diagnostic Radiology, Seoul National University College of Medicine, Seoul, Korea

Received: September 26, 1990;  Accepted: December 10, 1990.

Abstract

In order to find out the incidences of muscular ventricular septal defect and multiple ventricular septal defects in cases with isolated ventricular septal defect, tetralogy of Fallot, complete endocar- dial cushion defect, complete transposition of the great arteries, corrected transposition of the great arteries and double outlet right ventricle, a retrospective analysis of 620 left ventriculograms were performed. The surgical and echocardiographic findings were also considered to determine the location and number of the defects. The incidences of muscular defect were as follows; ventricular septal defect (2.1%), tetralogy of Fallot (3.1%), complete endocardial cushion defect (0.0%), complete transposition of the great arteries (12.1%), corrected transposition of the great arteries (12.5%) and double outlet right ventricle (9.1%). The incidences of multiple defects were as follows; ventricular septal defect (0.9%), tetralogy of Fallot (3.1%), complete transposition of the great arteries (9.1%), corrected transposition of the great arteries (6.3%) and double outlet right ventricle (9.1%). The incidence of muscular defect in isolated ventricular septal defect was lower than that of western countries. However the incidence of multiple defects in the transposition of the great arteries was not different from the result of the western study. All those who had defect(s) in muscular septum only hade good prognosis. Even in the cases with multiple defects, only a small proportion of the cases had surgically difficult lesions. As the incidence of multiple or muscular defect are very low in isolated ventricular septal defect and echocardigraphic accuracy of identifying muscular defect approaches 85%, the oriental patients with isolated ventricular septal defect may undergo surgical correction without invasive studies with neglible risk of residual muscular defect.

Keywords :multiple ventricular septal defect;Muscular ventricular septal defect