All issues > Volume 34(3); 1991

Original Article

J Korean Pediatr Soc. 1991;34(3):413-418. Published online March 31, 1991.

A case of xanthogranulomatous pyelonephritis.

Jin Oh Kim¹, Soo Young Cho¹, Joo Hyung Kim¹, Dae Yeol Lee¹, Jung Soo Kim¹

¹Department of Pediatrics, School of Medicine, Chonbuk National University, Chonju, Korea.

Received: July 9, 1990;  Accepted: September 26, 1990.

Abstract

Xanthogranulomatous pyelonephritis is an atypical form of severe chronic renal parenchymal infection, which can be mistaken for tumor or other inflammatory renal disease due to similar clinical manifestations. This disease was classified into three stages based on the extent of involvement of renal and adjacent tissue by the xanthogranulomatous process. In stage I (nephric), the characteristic xantho- granulomatous inflammatory process is confined to the kidney. The stage II lesion (perinephric) involves the renal parenchyma and Gerota’s fat, whereas the stage III lesion (paranephric) involves the renal parenchyma and its surrounding fat, with widespread retroperitoneal involvement. This disease is being predisposed by urinary obstruction, inappropriatly treated chronic urosepsis, lymphatic obstruction, abnormal immune reaction, diabetes melitus etc. We report here the 13 year old male patient suffering from Xanthogranulomatous pyelonephritis stage I who showed intermittent fever, left flank pain, and weight loss, which was confirmed by IVP, Abdominal CT, renal angiography, ultrasonography, and pathologic findings.

Keywords :Xanthogranulomatous pyelonephritis