All issues > Volume 34(2); 1991

Original Article

J Korean Pediatr Soc. 1991;34(2):261-266. Published online February 28, 1991.

A case of Caroli's disease.

Seong Hee Jung¹, Cheol Ho Chang¹, Han Tchah¹, Jeong Kee Seo¹, Kwi Won Park², In One Kim³, Kyung Mo Yeon³, Je Geun Chi⁴

¹Department of Pediatrics, Seoul National University College of Medicine, Seoul, Korea
²Department of Pediatric Surgery, Seoul National University College of Medicine, Seoul, Korea
³Department of Radiology, Seoul National University College of Medicine, Seoul, Korea
⁴Department of Pathology, Seoul National University College of Medicine, Seoul, Korea

Received: September 28, 1990;  Accepted: November 9, 1990.

Abstract

Caroli’s disease was first described by Caroli in 1958 and characterized by segmental cystic dilatation of the intrahepatic bile ducts. There is stasis of bile with stone formation in the dilatated ducts, giving rise to frequent attacks of pain and cholangitis. In the past, diagnosis of the Caroli’s disease is rarely established prior to operation and subsequent cholangiography. Recently, with ultrasonography, computerized tomography, radioisotope scan and percutaneous transhepatic cholangiography, it is possible to diagnose preoperatively and plan appro- priate intervention. We experienced a case of Caroli’s disease in a 8-year old girl who was admitted because of recurrent abdominal pain.

Keywords :Caroli's disease