All issues > Volume 33(12); 1990

Original Article

J Korean Pediatr Soc. 1990;33(12):1723-1728. Published online December 31, 1990.

A Case of Right Lung Agenesis Associated with Right Hemifacial Atrophy.

Jung Tak Kim¹, Young Mi Chung¹, Dong Goo Lee¹, Byeong Ju Jeoung¹, Kyu Earn Kim¹, Ki Young Lee¹, Jin Suk Suh²

¹Department of Pediatrics, College of Medicine, Yonsei University, Seoul, Korea
²Department of Diagnostic Radiology, College of Medicine, Yonsei University, Seoul, Korea

Received: June 14, 1990;  Accepted: September 11, 1990.

Abstract

Unilateral lung agenesis is a rare disease with associated anomalies of soft tissue, the musculos- keletal system, cardiovascular system and gastrointestinal system in 50-60% of cases. When associat- ed anomalies are absent, the disease may not be discovered during a lifetime, but in most of the cases, frequent respiratory infection or associated anomalies make it possible for diagnosis of the disease. Since early diagnosis is essential to prevent respiratory infection by careful respiratory physical therapy, it is continued by follow up. The authors experienced a case of right lung agenesis in 14-month-old female patient with right hemifacial atrophy who had suffered from frequent respiratory infections at least twice a month, and was diagnosed by chest X-ray, bronchogram, lung perfusion scan and chest C-T scan. Henceforth, we report the case together with references.

Keywords :Lung Agenesis