All issues > Volume 33(10); 1990

Original Article

J Korean Pediatr Soc. 1990;33(10):1434-1440. Published online October 31, 1990.

One Case of Recovery Phase of Aplastic Crisis in Hereditary Spherocytosis with Family History.

Eun Kyung Won¹, Dong Hyeon Kim¹, Ho Seung¹, Chang Hee Choi¹

¹Department of Pediatrics, Seoul Adventist Hospital, Seoul, Korea

Received: May 4, 1990;  Accepted: July 12, 1990.

Abstract

We experienced a case of hereditary spherocytosis patient who was in a recovery phase of aplastic crisis at the time of presentation. This was a 7 years old boy with complaints of pallor and intermit- tent abdominal pain. Asymptomatic jaundice was also found in the patient's grandfather and two maternal uncles. Patient’s mother had splenectomy due to hereditary spherocytosis. Diagnosis was made by morphology, osmotic fragility test, autohemolysis test of peripheral blood, and bone marrow examination. Splenectomy, as a choice of treatment, was done and remarkable symptomatic improvement was achieved.

Keywords :Hereditary spherocytosis, Aplastic crisis, Family history