All issues > Volume 33(8); 1990

Original Article

J Korean Pediatr Soc. 1990;33(8):1148-1154. Published online August 31, 1990.

Three cases of Lyphodystophia Centrifugalis Abdominalis Juvenilis.

Young Soo Chun¹, Byung Hee Kim¹, Young Youn Choi¹, Tai Ju Hwang¹

¹Department of Pediatrics, Chonnam University Medical School, Kwangju, Korea

Received: March 20, 1990;  Accepted: May 30, 1990.

Abstract

The Lipodystropia centrifugalis abdominalis juvenilis (LCAJ) is a skin disorder characterized by progressive, centrifugal loss of subcutaneous fat on inguinal and/or axillary region. The lesion has slightly red border and scaly change on it. But other skin manifestations or other organ involvements are not the feature of the disease. We have experienced 3 cases of LCAJ. They were 7 years 1 month old body, 9 years 1 month old girl and 7 years 1 month old girl, respectively. Physical examinations and laboratory findings were non-contributory except for depressed skin on inguinal region. Micro- scopical examination of the lesions showed decreased subcutaneous fat in all 3 cases. The 1st and 2nd cases belong to involutional group, while the 3rd case inflammatory group according to Peters and Winkelmann’s classification1^. During the one year follow up without treatment, the 1st and 2nd cases improved slightly, but the depressed lesion somewhat enlarged in the 3rd case. We report three cases of LCAJ with a review of literatures.

Keywords :Lipodystrophia centrifugalis abdominalis juvenilis